Duodenal atresia is the congenital absence or complete closure of a portion of the lumen of the duodenum. It causes increased levels of amniotic fluid during. Duodenal atresia or stenosis is a rare congenital digestive disorder that usually occurs for no apparent reason (sporadically). However, a few. A collection of disease information resources and questions answered by our Genetic and Rare Diseases Information Specialists for Duodenal atresia.

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The Center team will help care for you and your infant with duodenal atresia. It causes increased levels of amniotic fluid during pregnancy polyhydramnios and intestinal obstruction in newborn babies. J Med Assoc Thai.

Duodenal atresia

A child diagnosed with duodenal atresia will require an operation to address the problem and may stay in the hospital for several weeks.

Other investigations may be necessary after the baby is born. Years Published Twenty-five percent of their children may receive both normal genes, one from each parent, and will be genetically normal for xuodenum particular trait. Comparisons may be useful for a differential diagnosis: This causes an intestinal blockage.

Rare Disease Database

The Center coordinator will keep you in contact with the appropriate physicians and specialists as well as coordinating the care for you and your baby after delivery. The mother’s amniotic fluid and arresia growth of the baby will be monitored closely with ultrasound by the obstetrician.

The surgery is carried out through a small incision on the baby’s abdomen. Duodenal atresia occurs in 1 in every 5,—10, live births.

There are two theories as to why the abnormalities may occur. After birth, duodenal atresia may cause abdominal distension, especially of the upper abdomen. Duodenal atresia can result in an increase in the amniotic fluid around the baby known as polyhydramnios which may lead to an early delivery.

Treatment includes suctioning out any fluid that is trapped in the stomach, providing fluids intravenously, and surgical repair of the intestinal closure. Gastrointestinal tract disorders Congenital disorders of digestive system.


Although there are many other causes of hydramnios, this may be a first sign of a duodenal atresia. Because of this association, newborns are often tested for other problems such a heart defects. However, increasing amniotic fluid levels hydramnios does raise the chance for preterm delivery. Type of delivery – Babies with duodenal atresia usually do not need a cesarean delivery.

External links Down syndrome information. This is a procedure in which a connection is formed between the duodenum and the jejunum. Occasionally there may not be a complete atresia but a partial narrowing stenosis instead.

When the atresia is located in the first part of the duodenum, a gastrojejunostomy may be the treatment of choice. A duodenoduodenostomy is another surgical procedure sometimes used to create a connection or opening between the two portions of the divided duodenum.

Blood vessel defects in the embryo may cause the absence or closure of the duodenum by decreasing the blood supply in the affected area, or there may be an overgrowth of cells in the duodenum that obstruct the channel of the first part of the duodenum lumen occuring during the sixth or seventh week of fetal development. Anomalies associated with oesophageal atresia in Asians and Europeans.

Duodenal atresia or stenosis is a rare congenital digestive disorder that usually occurs for no apparent reason sporadically. Following discharge your baby will be seen in the outpatients department by members of the surgical team, where help and advice will be available to you.

Duodenal atresia is the congenital absence or complete closure of a portion of the lumen of the duodenum. Last Updated; August 22, The baby is likely to stay in the hospital for several weeks. It should be possible for the baby to grow quite normally on this form of feeding while the bowel is recovering. To contact Children’s Memorial Hermann Hospital, please fill out the form below.

Duodenal atresia – Wikipedia

Pyloric stenosis is a digestive disorder that may be apparent soon after birth or during the first few months of life. Duodenal atresia occurs between 1 in 1, and 1 in 5, live births. Appointment available in next 7 days.

Retrieved 16 September The duodenum is the bowel adjoining the stomach. The vomiting is described as “bilious”, because it contains bile acid. Duodenal atresias can occur as a complete or partial blockage of any portion of the duodenum. The guidelines issued are not intended to be prescriptive directions defining a single course of management and departure from the local guidelines should be fully documented in the patient’s case notes at the time the relevant decision is taken.


The Johns Hopkins University. Once bowel function returns, it will take a period of time before he or she can handle enough formula or breast milk to provide full nutrition.

Duodenal atresia

The defect in the duodenum may be located in the area where the pancreatic and bile ducts join as they open into the first part of the small intestines ampulla of Vater, or in the portion of the duodenum furthest from the opening of the ampulla of Vater. Oesophageal atresia and tracheo-oesophageal fistula TOF.

Your pregnancy will be closely monitored for complications. The overall outcomes for most duodenal atresias are excellent depending on the presence of additional problems. This line is usually placed in a small vein in an arm or leg and fed through into a large vein. Milk feeds will be slowly introduced and increased, as the baby is able to tolerate them.

The baby will receive all of the calories necessary to grow until he or she can be fed through the intestinal tract. The development of forceful vomiting projectile immediately after eating or when the stomach is filled is one of the first symptoms. Standard Therapies Duodenal atresia may be recognized through ultrasound by the presence of a “double bubble” which can be seen in the abdominal area. This is a procedure in which there is a surgical creation of a connection between the stomach and jejunum bypassing the obstruction.

Comparisons may be useful for a differential diagnosis:.